Juvenile xanthogranuloma - Xanthogranuloma Òganach
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References
Tha Juvenile xanthogranuloma (JXG) na staid gu math cumanta agus an seòrsa non-Langerhans cell histiocytic disorder as trice ann an cloinn. Ann an timcheall air 75% de chùisean, tha na leòintean sin a ‘nochdadh taobh a-staigh a’ chiad bhliadhna de bheatha, agus tha còrr air 15-20% de dh’euslaintich gan faighinn bho àm breith. Ged a tha e tearc ann an inbhich, bidh JXG mar as trice a’ tachairt mar as trice ann an daoine anmoch anns na ficheadan is tritheadan aca, agus chan eil ach aon leòn aig a’ mhòr-chuid de dh’ euslaintich inbheach. Gu clionaigeach, tha e a 'nochdadh mar chnapan no cnapan cruaidh buidhe-orains-donn singilte no iomadach, gu h-àraidh air an aghaidh, amhach, agus corp àrd. Tha leòintean beòil neo-àbhaisteach ach faodaidh iad nochdadh mar chnap buidhe air taobhan a 'chànain no ann an àiteachan eile sa bheul, is dòcha a' leantainn gu ulcers agus bleeding. Mar as trice chan eil lotan craicinn ag adhbhrachadh comharraidhean agus bidh iad buailteach a dhol air falbh leotha fhèin thar grunn bhliadhnaichean. Ged a tha e tearc, is e com-pàirt sùla an cùis as cumanta taobh a-muigh a 'chraicinn, agus an uairsin com-pàirt sgamhain. Mar as trice chan eil buaidh aig Ocular JXG ach air aon shùil agus bidh e a’ tachairt ann an nas lugha na 0. 5 % de dh’ euslaintich, ged a tha grunn lotan craiceann aig timcheall air 40% den fheadhainn le com-pàirt sùla nuair a thèid an lorg.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Juvenile xanthogranuloma (JXG) is a relatively common entity and is the most common form of non-Langerhans cell histiocytic disorder of childhood., It is estimated that in 75% of cases, lesions appear during the first year of life, with >15-20% of patients having lesions at birth. JXG is rare in adults, with a peak incidence in the late twenties to thirties. The majority of adult patients have solitary lesions. Typically, the clinical presentation consists of solitary or multiple yellow-orange-brown firm papules or nodules. The most common locations are the face, neck, and upper torso. Oral lesions are rare and often occur as a yellow nodule on the lateral aspects of the tongue. Oral lesions can also arise on the gingival, buccal mucosa, and midline hard palate and may ulcerate and bleed. Cutaneous lesions are usually asymptomatic, and most lesions spontaneously involute over the course of several years. Although occurring rarely, ocular involvement is the most common extracutaneous site involved, followed by the lungs. Ocular JXG is nearly always unilateral and develops in less than 0.5% of patients. Approximately 40% of patients with ocular JXG, however, have multiple cutaneous lesions at the time of diagnosis.
Tha Juvenile xanthogranulomas (JXGs) nan galairean neo-chumanta a tha nam pàirt de roinn nas motha de non-Langerhans cell histiocytoses. Mar as trice bidh iad a 'nochdadh mar aon no barrachd cnapan dearg no buidhe, gu tric air an ceann no amhaich. Bidh a’ mhòr-chuid de JXG a’ fàs aig àm breith no taobh a-staigh a’ chiad bhliadhna de bheatha. Ged a tha e neo-àbhaisteach, uaireannan faodaidh iad buaidh a thoirt air raointean taobh a-muigh a 'chraicinn, le com-pàirt sùla mar rudeigin ri choimhead a rèir an litreachais a th' ann mar-thà. San fharsaingeachd, bidh JXGs air a 'chraiceann a' falbh leotha fhèin agus mar as trice chan fheum iad leigheas.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Juvenile xanthogranulomas (JXGs) are uncommon, benign diseases that are part of a larger category of non-Langerhans cell histiocytoses. They typically show up as one or more red or yellowish lumps, often found on the head or neck. Most JXGs develop either at birth or within the first year of life. While it's unusual, sometimes they can affect areas beyond the skin, with eye involvement being something to watch for according to existing literature. Generally, JXGs on the skin go away on their own and typically don't need treatment.
Bidh leòn sùla a’ nochdadh ann an suas ri 10% de dhaoine le JXG agus dh’ fhaodadh sin buaidh a thoirt air an lèirsinn aca. Ged a bhios leòintean gearraidh mar as trice a 'dol à sealladh gu neo-iomchaidh, is ann ainneamh a bhios lotan sùla a' fàs nas fheàrr agus feumar leigheas.